Tabriz University of Medical Sciences Journal of Cardiovascular and Thoracic Research 2008-5117 4 4 2012 10 30 Isolated Right Sided Anomalous Pulmonary Venous Connection Associated with Significant Right ventricular Enlargement and Intact Interatrial Septum 123 124 10.5681/jcvtr.2012.029 EN Zahra Ojaghi Haghigh Anita Sadeghpour Azin Alizadehasl Journal Article 10.5681/jcvtr.2012.029 2012 09 02 Partial anomalous pulmonary venous connection (PAPVC) is a very rare congenital heart disease where one or more of the pulmonary veins are connected to the venous circulation. Although initially suspected with inexplicable right ventricular enlargement on transthoracic echocardiography, other modalities such as transesophageal echocardiography, CT angiography or cardiac Magnetic resonance (CMR) imaging are able to diagnosis the anatomical abnormalities. We present a 29-year-old female with moderate right ventricular enlargement and isolated right upper and middle pulmonary vein anomalous return to superior vena cava.