Tabriz University of Medical Sciences Journal of Cardiovascular and Thoracic Research 2008-5117 16 3 2024 09 20 Unicuspid unicommissural aortic valve 198 199 10.34172/jcvtr.33170 EN Nataraju Komalamma Girish https://orcid.org/0009-0001-5634-5388 Niraj Nirmal Pandey https://orcid.org/0000-0001-6786-8304 Priya Jagia Sandeep Singh Journal Article 10.34172/jcvtr.33170 2024 05 02 2024 09 06 We describe a case of a 30-year-old woman with gradually increasing dyspnoea on exertion where CT angiography revealed a unicuspid unicommissural morphology of the aortic valve. The present report highlights the anatomical and embryological aspects of this rare anatomical variant as well as the associated cardiovascular abnormalities.